Treatment of Pan-craniofacial Polyostotic Fibrodysplasia not Involving Maxilla: Mandible Reconstruction with Free Fibular Bone Flap. |
Seong Jun Cheon, Kyung Suk Lee |
Department of Plastic and Reconstructive Surgery, College of Medicine, Gyeongsang National University, Jinju, Korea. opensound@han mail.net |
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Abstract |
Fibrous dysplasia is a benign pathologic condition of bone and causes facial deformity as well as functional problems.
The monostotic form of the disease is much more common(70-80 percent) than the polyostotic variety (20-30 percent). In craniofacial fibrous dysplasia, craniofacial involvement occurs in 10-30 percent of monostotic and 50 percent of polyostotic patients. Frontal, sphenoid, ethmoid, and maxilla bones are frequently involved. Jaw involvement may involve a solitary lesion, but nonetheless in more common in the maxilla than in the mandible. We report a case of mandible reconstruction of pan-craniofacial polyostotic fibrous dysplasia that do not involve maxilla. In operation, extensive hemimandibulectomy was done and fibular bone free flap was done for mandible reconstruction. Postoperative 6 months later, focal osteomyelitis was seen in mandible angle. We removed mini-plate and screw and illiac cancellous bone graft was performed. 3 months after second operation, wound healing was uneventful and we have a functionally and cosmetically good outcome. |
Keywords:
Fibrous dysplasia; Mandible reconstruction; Fibular bone free flap |
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